PEComa of the lung
By: Dr. Sanket Mehta
Authors: R Vijayabhaskar, Kedar K Deodhar, CS Pramesh, Rajesh C Mistry
Category: Parotid and Thyroid Surgeries
Start: January 1, 2010
Perivascular epithelioid cell tumor (PEComa), also called clear cell ”sugar” tumor of the lung, is a rare benign tumor arising from perivascular epithelioid cells (PECs). We report a case of a 15-year-old boy who presented with right lower lobe lesion which turned out to be a clear cell tumor of the lung.
An [18F]-fluoro-2-deoxy-D-glucose (FDG) – positron emission tomography (PET) scan revealed mild FDG uptake in the lung lesion (SUV<1) with no active uptake elsewhere in the body. We discuss the clinical, radiologic and immunohistochemical features of clear cell ”sugar” tumor of lung and compare them with published literature.