PEComa of the lung

By: Dr. Sanket Mehta
Authors: R Vijayabhaskar, Kedar K Deodhar, CS Pramesh, Rajesh C Mistry
Category: Parotid and Thyroid Surgeries
Start: January 1, 2010
DOI: 10.4103/0973-1482;year=2010;volume=6;issue=1;spage=109;epage=111;aulast=Vijayabhaskar.63548


Perivascular epithelioid cell tumor (PEComa), also called clear cell ”sugar” tumor of the lung, is a rare benign tumor arising from perivascular epithelioid cells (PECs). We report a case of a 15-year-old boy who presented with right lower lobe lesion which turned out to be a clear cell tumor of the lung.

An [18F]-fluoro-2-deoxy-D-glucose (FDG) – positron emission tomography (PET) scan revealed mild FDG uptake in the lung lesion (SUV<1) with no active uptake elsewhere in the body. We discuss the clinical, radiologic and immunohistochemical features of clear cell ”sugar” tumor of lung and compare them with published literature.

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